The syndrome associated with deficiency of Dermatan sulfate, heparan sulfate, chondroitin 4-sulfate and chondroitin 6-sulfate is
Disease name Abbretion Enzyme Defective GaG(s) affected Symptoms Sly syndrome MPS VII b-Glucuronidase Dermatan sulfate, heparan sulfate, chondroitin 4-sulfate, chondroitin 6-sulfate Skeletal dysplasia, sho stature, hepatomegaly, cloudy cornea Reference: Harper; 30th edition; Page no:639; Table: 50-8
Hunter syndrome
Morquio syndrome B
Sly syndrome
Hurler syndrome
Metabolism of carbohydrate