Branching enzyme deficiency is seen in
Type Name Enzyme Deficiency Clinical Features IV Amylopectinosis, Andersen disease Branching enzyme Hepatosplenomegaly Accumulation of polysaccharide with few branch points Death from hea or liver failure before age 5 Reference: Harper; 30th edition; Table: 18-2; Page no: 179
Andersen disease
McArdle's syndrome
Cori disease
Von Gierke disease
Metabolism of carbohydrate