A pt presented with pulsating varicose veins of the lower limb. Most probable diagnosis is
Ans. is 'a' ie Klippel-Trenaunay Syndrome Klippel- Trenaunay Syndrome :is characterized byCongenital AV fistulasCutaneous hemangiomasVaricose veinsHyperophy of involved extremityAbsence of deep venous system (so pathological superficial veins should not be removed without evidence of an intact deep system)*Another syndrome closely associated with A-V malformations is:Kasabach-Merritt syndrome characterised by:- thrombocytopenia* and- hemorrhagic manifestation *- d/t trapping & destruction of platelets* within the AV malformations*.
Klippel Trenaunay syndrome
Tricuspid regurgitation
DVT
Right ventricular failure