Features of Peutz-Jeghers syndrome are all except
Peutz Jeghers syndrome is an autosomal dominant defect, characterised by hamaomatous intestinal polyposis and melanotic pigmentation of lips , mouth and genitalia. It DONOT UNDERGO MALIGNANT TRANSFORMATION unless a coexistant adenoma present. Reference : Harsh Mohan textbook of pathology, 7th edition.Pg no.566
Autosomal dominant
Mucocutaneous pigmentation
Hamaomatous polyp
High risk of malignacy
Haematology