A 5 year boy presented with massive hematemesis. He is not febrile. Per abdomen examination revealed massive splenomegaly without hepatomegaly. Most probable diagnosis would be:
Ans. B. Extrahepatic portal venous obstructionExtrahepatic obstruction is the most common cause of portal hypertension in children. Patients with extrahepatic portal venous obstruction usually present at about 5-6 years with hematemesis with or without melena. Splenomegaly is almost universal in patients with EHPVO and size of spleen is usually dependent on the duration of the illness. Liver is usually normal in size. Ascites is usually rare.
Non-cirrhotic portal fibrosis
Extrahepatic portal venous obstruction
Budd-Chiari syndrome
Hepatic carcinoma
Gastro Intestinal System