True about Peutz-Jegher's syndrome:
Peutz Jegher Syndrome: Autosomal dominant Characterized by mucocutaneous pigmentation and extensive GI hamaomatous polyposis Life time risk of cancer- 47-93%
Pigmentary changes in skin and mucous membrane around mouth
Adenomatous polyp in intestine
Most common of pattern inheritance is autosomal recessive
20-30% premalignant
Disorders of Gastrointestinal System Including Diarrhea