2 month old infant is presented with failure to thrive,recurrent emesis, hepatospleomegaly and adrenal insufficiency, Adrenal calcification is noted radio logically, What is the most probable diagnosis?
Wolman disease is lipid disorder caused by deficiency of lysosomal acid lipase.
Presents with above clinical feature.
Pneochromocytoma
Addison disease
Wolman disease
Adrenal disease