'Shepherd's crook' deformity of the proximal femur seen in
(Fibrous dysplasia) (227-M) (174-75-Abley 8th)FIBROUS DYSPLASIA is a developmental disorder in which areas of trabecular bone are replaced by cellular Fibrous tissue containing flecks of osteoid and woven bone* ** Occasionally the bone disorders is associated with "cafe-au-lait " patches on the skin and (in girls) precocious sexual development (Albright's syndrome)* * Malignant transformation to fibrosarcoma occurs in 5-10% of patients with polystotic lesions, but only rarely in monostotic lesionsX ray shows radiolucent 'cystic ' areas in the metaphysis or shaft because they contain fibrous tissue with diffuse spots of immature bone, the lucent patches typically have a slightly hazy or 'ground glass' appearanceThe weight bearing bones may be bent and one of the classic features is the 'shepherd's crook' deformity of the proximal femur
Fibrous dysplasia
Chondroblastoma
Osteochondroma
Aneurysmal bonecyst
Bone Tumour