Which one of the following statements, concerning persistent hyperplastic primary vitreous (PHPV) is not true?
B i.e. Visual prognosis is usually good Persistent Hyperplastic Primary Vitreous (PHPV) It is persistence of the primary viterous & hyaloid aerial system. Almost always unilateralQ (-90%) Presents as white pupillary reflex in the new born (congenital leukocoria)Q It is usually associated with - CataractQ - Glaucoma - Long & extended ciliary processes because of pull from contracted retrolental tissue. - MicrophthalmosQ - Intraocular haemorrhage - Tractional RD Investigations: USG & CT Scan D/D with Retinoblastoma on the basis of microphthalmia & elongated ciliary processes If diagnosed early, T/T is aspiration of lens, excision of retrolental membrane and vitrectomy Visual prognosis is poorQ.
It is generally unilateral
Visual prognosis is usually good
It may calcify
It is most easily differentiated from retinoblastoma by the presence of exophthalmos or cataract.