Zellweger syndrome is due to defect in-
Ans. is 'b' i.e., Fatty acid oxidation in peroxisomes o Zellweger Syndrome is a rare inborn error of peroxisomal fatty acid oxidation due to absence of functional peroxisomes in all tissues. As a result, the long chain fatty acids are not oxidized in peroxisomes and accumulate in tissues particularly in brain, liver, kidney and muscle and usually result in death by age six.
Fatty acid synthesis in cytosol
Fatty acid oxidation in peroxisomes
Fatty acid oxidation in mitochondria
Fatty acid oxidation in smooth ER
Lipid Oxidation and Synthesis