Which of the following amino acid is excreted in urine in maple syrup urine disease
In maple syrup urine disease there is the excretion of branched chain amino acids (isoleucine, leucine, valine) and their keto acids (α -keto β-methyl valerate, α-ketoisocaproate, α-ketoisovalerate) in the urine.
Tryptophan
Phenylalanine
Leucine
Arginine