Maple syrup urine disease is due accumulation of
Maple syrup urine disease is also called branched-chain ketonuria The basic defect is deficient decarboxylation of branched-chain ketoacids.Ref: DM Vasudevan - Textbook of Biochemistry, 7th edition, page no: 230
Phenylalanine
Tyrosine
Branched chain amino acids
Tryptophan
Metabolism of protein and amino acid