True about primary lymphoedema
<p> Lymphoedema Accumulation of fluid in extracellular and extravascular fluid compament , commonly in subcutaneous tissue. Classification: 1. Primary - without any identifiable disease. 2. Secondary- acquired due to definitive cause. Primary lymphoedema:- Affects commonly females. Common in lower limb and left side. It can be familial , syndromic ( Turners , Klinefelter&;s , Down&;s, Klipple Trenauy weber) It can be 1. Lymphoedema congenital : present at bih (<2yrs). Familial type is called Nonne- Milroy disease. 2. Lymphoedema praecox- present at pubey (2-35 years). Familial type is called Letessier- Meige&;s syndrome. 3. Lymphoedema tarda- present in adult life after 35 years. Complications: Skin thickening, abscess, maggot formation. Recurrent cellulitis Lymphangiosarcoma Recurrent streptococcal infection. {Reference: SRB&;s manual of surgery, 5th edition , page no. 247}
Lymphangiosarcoma may occur
A/W Milroy's disease
Onset b/w 2-35 years indicates lymphoedema tarda
Onset > 35 years indicates praecox variety
Vascular surgery