Essential fructosuria is due to the deficiency of which enzyme?
Ans. (c) FructokinaseRef: Harper, pg. 169"Deficiencies in the enzymes of fructose and galactose metabolism lead to essential fructosuria and galactosemias""Lack of hepatic fructokinase causes essential fructosuria, and absence of hepatic aldolase B, which cleaves fructose 1-phosphate,leads to hereditary fructose intolerance"Metabolism of fructose. Aldolase A is found in all tissues, whereas aldolase B is the predominant form in liver. (not found in liver)
Aldolase A
Aldolase B
Fructokinase
Glucokinase
Carbohydrates