In all the following metabolic disorders, clinical features are seen due to accumulation of toxic compounds EXCEPT?
Clinical features are seen due to accumulation of toxic compounds in: Phenylketonuria, Maple syrup urine disease, Urea cycle defects, organic acidurias & porphyrias. Mitochondrial disorders involve defects of energy production or utilisation in various organs of body.
Phenylketonuria
Maple syrup urine disease
Urea cycle defects
Mitochondrial disorders
Disorders of Amino acid Metabolism