Which of the following statement about VHL syndrome is true?
Ans. (b) Craniospinal hemangioblastoma are commonRef: Sabiston 19th edition page 708Von Hippel Lindau Syndrome:* Autosomal dominant* Multiple vascular tumors in many organs* Hemangioblastomas of Retina and CNS* Renal cysts, Cysts in Epididymis, Liver and Pancreas* Clear cell RCC* Pheochromocytoma* Pancreatic endocrine tumors* Adrenal cancers* Polycythemia is a characteristic feature of VHL due to erythropoietin production by hemangioblastoma
Multiple tumors are rarely seen
Craniospinal hemangioblastoma are common
Supratentorial tumors are common
Tumors of Schwann cells are common
Nervous System