Which of the following is a characteristic feature of Moyamoya disease?
Answer- B. Absence of vascular inflammationOcclusive disease involving large intracranial aeries, especially the distal internal carotid aery and the stem of the middle cerebral and anterior cerebral aery.The lenticulostriate aeries develop a rich collateral circulation around the occlusive lesion, which gives the impression of a 'puff of smoke" ( moyamoya in ]apanese) on conventional x-ray angiographyOccurs mainly in Asian children or young adults.Surgical bypass of extracranial carotid aeries to the dura or MCAs may prevent stroke and hemorrhage.
Involvement of proximal internal carotid aery
Absence of vascular inflammation
Patients can be given anticoagulants without any additional risk
Surgical bypass from internal carotid aery to middle meningeal aery can be a treatment.