All the following are features of Von Gierke disease except
Type name Enzyme Deficiency Clinical Features Ia Von Gierke disease Glucose-6-phosphatase Glycogen accumulation in liver and renal tubule cells Hypoglycemia Lactic acidemia Ketosis Hyperlipidemia Reference: Harper; 30th edition; Table: 18-2; Page no: 179
Hypoglycemia
Lactic acidosis
Hyperlipidemia
Muscle hypotonia
Metabolism of carbohydrate