In argininosuccinase deficiency, what should be supplemented to continue the urea cyce -
Ans. is 'b' i.e., Arginine o Argininosuccinase (argininosu coin ate lyase) catalyses the cleavage of arginiosuccinate into arginine and fumarate.o Thus, in argininosuccinase deficiency arginine cannat be produced.o Supplementation with arginine base helps replenish this amino acid.
Aspartate
Arginine
Citrull in
Argininosuccinate
Amino Acid Metabolism