A teenage girl is diagnosed with Mayer-Rokitansky-Kuster-Hauser syndrome. It consists of:
In mullerian aplasia or mullerian agenesis or Mayer-Rokitansky-Kuster-Hauser syndrome, patients have a shallow vaginal pouch, only measuring 1 to 2 inches deep. In addition, the uterus, cervix, and upper pa of the vagina are absent. Typically, a poion of the distal fallopian tubes are present. Also, normal ovaries are seen. Ref: Hoffman B.L., Schorge J.O., Schaffer J.I., Halvorson L.M., Bradshaw K.D., Cunningham F.G., Calver L.E. (2012). Chapter 18. Anatomic Disorders. In B.L. Hoffman, J.O. Schorge, J.I. Schaffer, L.M. Halvorson, K.D. Bradshaw, F.G. Cunningham, L.E. Calver (Eds), Williams Gynecology, 2e.
Ovaries, uterus, fallopian tubes are present
Uterus absent, distal fallopian tube, ovaries are present
Uterus, tubes and ovaries are absent
Uterus present tubes and ovaries absent