Which is involved in transpo of long chain acyl-CoA in mitochondria?
In humans carnitine is synthesized from protein-derived trimethyllysine in liver, brain and kidney.Muscles take up carnitine from the blood in an exchange-diffusion process with endogenous deoxycarnitine, the immediate precursor of carnitine.Besides catalysing the transpo of long-chain acyl groups in mitochondria, carnitine is necessary for the expo of intramitochondrially produced sho-chain acyl residues and for the trapping and the elimination of unphysiological compounds (benzoic, pivalic, valproic acids etc.).
Ornithine
Xanthine
Carnitine
Albumin