13-year-old female child presented with recurrent sinusitis fever, ahralgia, respiratory distress, Hematuria and hypeension. Renal biopsy showed necrotizing granuloma. The anti proteinase-3 ANCA was positive. The most likely diagnosis is:
Respiratory & Renal involvement along with positive c-ANCA (Anti Proteinase 3) indicates Wegener's Granulomatosis
Polyaeritis Nodosa
Wegener's granulomatosis
Microscopic polyangiitis
Churg-Strauss syndrome
Vasculitic Disorders in Children