Bilateral Renal cell carcimoma is seen in
VHL syndrome: Autosomal dominant cancer syndrome, characterized by: Cerebellar hemangioblastomas Retinal angiomas Clear cell RCC Pheochromocytoma Cysts in various organs. Patients of VHL disease have germline mutations of tumor suppressor VHL gene located on chromosome 3p, commonly as homozygous loss of the VHL gene. About 35% of cases of VHL develop RCC. Ref: Ram Das Nayak 2nd edition page no: 633
Eagle Barett's syndrome
Beckwith Weideman syndrome
Von Hippel Lindau disease
Bilateral Angiomyolipoma
Urinary tract