Most common cause of Budd-Chiari syndrome is:
Primary Budd-Chiari syndrome (75%): thrombosis of the hepatic vein Secondary Budd-Chiari syndrome (25%): compression of the hepatic vein by an outside structure (e.g. a tumor) The cause for the disease cannot be found in about half of the patients. Hepatic vein thrombosis is associated with the following in decreasing order of frequency: Polycythemia vera": is a primary,absolute erythrocytosis. The EPO levels are suppressed causing alow to normal EPO in the blood. Pregnancy Post paum state Use of oral contraceptives Paroxysmal nocturnal hemoglobinuria Hepatocellular carcinoma Lupus anticoagulant
Hepatic vein valves
Hypercoagulable state in Nephrotic syndrome
PNH
Polycythemia vera
Budd chiari syndrome & Pancreatitis