Which epileptic syndrome is associated with left hemispheric atrophy in child?
All the above options are epileptic syndromes, among these only Dyke Davidson Masson syndrome have characteristic Childhood Cerebral Hemiatrophy features. Dyke Davidson Masson syndrome: Hemiatrophy or hypoplasia of unilateral cerebral hemisphere resulting from brain insult in fetal or early childhood period with compensatory ipsilateral calvarial hyperophy Insult could be vascular, congenital or acquired ischemic disease, trauma or inflammation In-utero gestational vascular occlusion involving middle cerebral vascular territory or coarctation of mid-aoic arch may decrease carotid aerial flow Dravet Syndrome- prolonged seizures, psychomotor delay, ataxia. It is characterized by cognitive impairment, behavioral disorders, and motor deficits. Lennox Gastaut syndrome- seizures, cognitive dysfunction, and EEG findings (slow spike wave). West Syndrome- epileptic/infantile spasms, abnormal brain wave patterns (hypsarrhythmia) and intellectual disability.
Dravet Syndrome
Dyke Davidson Masson syndrome
Lennox Gastaut syndrome
West Syndrome
JIPMER 2019