All the following Lipidoses are inherited as Autosomal Recessive Except
FABRY DISEASE This disease is an X-linked inborn error of glycosphingolipid metabolism caused by the absent or markedly deficient activity of a-galactosidase A (a-gal A).Reference: Nelson Textbook of Paediatrics; 20th edition; Chapter 86; Defects in Metabolism of Lipids
Fabry
Krabbe
Gaucher
Taysachs
Metabolic disorders