All of the following are true about Childhood Polycystic Kidney Disease, Except.
Answer is B (Presentation is Unilateral): The presentation in Polycystic disease of kidney is characteristically bilateral - The bilateral enlargement can hardly be mistaken on routine examination - Bailey - USG and CT show multiple cysts in both kidneys - Bailey The disease may present at any age but the most common age ofpresentation is in the 3rd or 4th decade. Both the kidney are grossly enlarged and situated with multiple cysts. Intracranial berry aneurysms are seen in 5-10 % of patients.
Autosomal Dominant
Pulmonary Hypoplasia may be seen
Renal cysts are present at bih
Congenital Hepatic fibrosis may be seen