In late stages of systemic sclerosis may have all the given features, EXCEPT:
Late stages of limited systemic sclerosis patients may develop Pulmonary aerial hypeension (PAH), Interstitial lung disease, Hypothyroidism, Primary biliary cirrhosis Raynaud's phenomenon and other typical features of systemic sclerosis occur in the absence of detectable skin thickening in some patients. This syndrome is been termed SSc sine scleroderma. Ref: Harrison, E-18, P- 2757.
Pulmonary aery hypeension
Interstitial lung diserase
Primary biliary cirrhosis
Primary sclerosing cholangitis