Mousy odour urine is seen in
Mousy order urine is seen in phenylketonuria due to the presence of excessive phenylalanine and its metabolites.Mousy body odour is also present due to the excretion of phenyl lactic acid,its metabolite through sweat. Reference:Essential pediatrics-Ghai,8th edition,page no:652.
Maple syrup urine
Phenylketonuria
Isovalericacidria
Cystinuria
Metabolic disorders