All is true about von Hippel Lindau syndrome except:
C i.e. Tumors of Schwann cells are common Von Hippel-Lindau (VHL) syndrome is associated with multiple hemangioblastomasQ of infratentorial craniospinal axis, retina and pancreas. Supratentorial HB are uncommonQ.
Hemangioblastomas seen in craniospinal axis
Multiple tumors common
Tumors of Schwann cells are common
Supratentorial lesions are uncommon