Von Gierke&;s occurs due to deficiency of
Glycogen storage disease type I (GSD I) or von Gierke&;s disease, is the most common of the glycogen storage disease. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase and has an incidence in the American population of approximately 1 in 100,000 bihs.Ref: DM Vasudevan, 7th edition, page no: 128
Glucose-6-phosphatase
Liver Phosphorylase
Muscle phosphorylase
Debranching enzyme
Metabolism of carbohydrate