True about 'Tetralogy of Fallot' (TOF) are all of the following EXCEPT?
TETRALOGY OF FALLOT: --> MC congenital cyanotic hea disease in children --> Contain 4 COMPONENTS: 1. Large, unrestricted VSD 2. Pulmonary infundibular stenosis 3. Overriding aoa 4. Right ventricular hyperophy --> CLINICAL FEATURES: Cyanosis Clubbing Polycythemia Cyanotic spells Hea failure is not seen in TOF, unless it is complicated by Anemia /Infective endocarditis /Myocarditis / Systemic hypeension Severity of cyanosis is directly propoional to the severity of pulmonary stenosis; while intensity of murmur is inversly propoional to severity of pulmonary stenosis During cyanotic spell, murmur decreases or becomes absent -Ostium primum type ASD: It is situated in the lower poion of atrial septum and overlies mitral and tricuspid valves. Left axis detion is seen in ostium primum ASD due to RV conduction defect. - Ostium secundum is most common type of ASD - SYNDROMES ASSOCIATED WITH ASD 1. Pierre Robin Sequence 2. TAR Syndrome 3. Fetal Alcohol syndrome 4. Ehler Danlos Syndrome 5. Down Syndrome 6. Holt-Oram syndrome 7. Ellis van Creveld Syndrome 8. Rubinstein Taybi syndrome
It is the most common congenital cyanotic hea disease in children
Severity of disease depends on the severity of pulmonary stenosis
Atrial septal defect is one of the components of TOF
Boot shaped hea is seen on chest X ray
Acyanotic congenital hea diseases