Wilms' tumor is the most common primary malignant tumor of the kidney in children. Wilms' tumor is associated with all of the following conditions, EXCEPT:
Symptoms of Wilms' tumor include asymptomatic mass in the flank or upper abdomen, hypeension, hematuria, obstipation, and weight loss. Genetic predispositions of Wilms' tumor include the WAGR syndrome, which consists of Wilms' tumor, aniridia, genitourinary abnormalities, and mental retardation. In addition, there is an increased incidence of Wilms' tumor in ceain overgrowth conditions, paicularly Beckwith-Wiedemann syndrome and hemihyperophy. Genitourinary abnormalities such as hypospadias, cryptorchidism, and renal fusion. Ref: Hackam D.J., Grikscheit T.C., Wang K.S., Newman K.D., Ford H.R. (2010). Chapter 39. Pediatric Surgery. In F.C. Brunicardi, D.K. Andersen, T.R. Billiar, D.L. Dunn, J.G. Hunter, J.B. Matthews, R.E. Pollock (Eds), Schwaz's Principles of Surgery, 9e.
Hemihyperophy
Aniridia
Hypeension
Bilateral polycystic kidney disease