A patient presents with LVII. and pulmonary complications. ECG, shows left axis detion. Most likely diagnosis is -
Ans. is 'b' i.e., Tricuspid Atresia Congenital absence of tricuspid valve is called tricuspid atresia. Haemodynamics : The inflow poion of R.V. is hypoplastic The systemic venous blood coming to R.A. exits by way of a patent foramen ovale or an ASD. A VSD provides communication between L.V. and outflow poion of R.V. o The L.V. thus maintains both the systemic and pulmonary circulation. The saturation of blood in the pulmonary aery and aoa is identical --> Because unoxygenated blood from right atrium mixes with oxygenated blood into left atrium. The pulmonary blood flow is dependent on size of VSD --> Smaller the VSD, less the pulmoanry blood flow. Clinical features : Child is cyanotic from bih Anoxic spells and squatting may be present. Features suggestive of tricuspid atresia : a) L.V. type of apical impulse b) Prominent large 'a' waves c) Enlarged liver with presystolic pulsations (a waves) d) ECG characterised by Left axis detion and Left ventricular hyperophy.
TOF
Tricuspid atresia
TAPVC
VSD