Primary CNS lymphomas are extranodal, malignant non-Hodgkin lymphomas of the diffuse large B-cell type that are confined to the brain, eyes, leptomeninges, or spinal cord, in the absence of systemic lymphoma. Primary CNS lymphomas are estimated to account for up to 1% of all lymphomas, 4–6% of all extranodal lymphomas, and about 3% of all CNS tumours. After a continuous rise in the incidence of primary CNS lymphoma during the 1980s and 1990s, epidemiological data in high-income countries show a decrease in incidence, particularly among young patients with AIDS.
Primary central nervous system lymphoma classification
Primary central nervous system lymphoma epidemiology and demographics
Hodgkin's lymphoma classification
Primary central nervous system lymphoma MRI
Autoimmune lymphoproliferative syndrome classification
Langerhans cell histiocytosis classification
Burkitt's lymphoma classification
B-cell lymphoma classification