<unk>  is an acquired complete heart block due to idiopathic fibrosis and calcification of the electrical conduction system of the heart.<unk>  is most commonly seen in the elderly and is often described as senile degeneration of the conduction system.
One form has been associated with SCN5A.<unk> 's Syndrome is a rare, progressive cardiac conduction defect (PCCD) due to myocardial fibrosis first described by Maurice<unk>  in 1964. This condition, proposed to start in the fourth decade of life, involves a sclerotic fibro-fatty degeneration of the Bundle of His and Purkinje fibers, which<unk>  proposed caused increasing AV delay with age. With the prevalence of electrocardiogram (ECG) use in the emergency department (ED) for cardiac- and non-cardiac complaints, dysrhythmias can be incidentally found and confuse diagnosis and disposition. We highlight the case of an 84-year-old male who presented to the ED for acute onset of diffuse facial paresthesias with elevated blood pressure at home and was found to be significantly bradycardic on initial evaluation. On serial ECGs, the conduction rhythm changed from an initial new first-degree atrioventricular (AV) block with left bundle branch block (LBBB), to a later first-degree AV block without LBBB. Cardiology was consulted. Serial ECGs demonstrated an evolving conduction block arrhythmia consistent with<unk> 's Syndrome. Here we describe a case of symptomatic bradycardia found to be consistent with<unk> 's Syndrome.
Lev's disease
Darier's disease
Jeune's disease
Kienbock's disease
Bowen’s disease
Dent's disease
Bowen's disease
Grover's disease