<unk>  is a rare mesenchymal soft tissue tumor. It often occurs in the extremities of young people.  Diagnosis is often delayed because of the unusual nature of the tumor.<unk>  was first discovered by Dr. J. Laskowski, a polish doctor, in 1961 following the description of a clinical entity called<unk>  aponeuroticum due to the involvement of aponeurosis. Enzinger coined the term<unk>  in 1970. Mutations in the SMARCB1 gene cause<unk> .<unk>  must be differentiated from synovial<unk> , wart, ganglion cyst, rhabdomyosarcoma, and clear cell<unk> . Irregular (or nodular) lesions below the skin surface are the major symptom of<unk> . The symptoms of<unk>  usually develop in the second decade of life and start with symptoms such as mass.<unk>  has a tendency for lymph node metastasis. The most common sites of<unk>  metastasis include lungs, lymph nodes, and scalp. Common complications of<unk>  include metastasis, nerve compression, and numbness. The prognosis of<unk>  is good for females. The predominant therapy for<unk>  is surgical resection. Adjunctive chemotherapy, radiation, and chemoradiation may be required.
Epithelioid sarcoma
Reticulum cell sarcoma
Alveolar soft part sarcoma
Granulocytic sarcoma
Adenomatoid tumor
Angiosarcoma
Sarcoma
Malignant fibrous histiocytoma