<unk>  is a very rare tumor characterized by the presence of abundant mucus in the abdominal cavity, consisting of intraperitoneal mucinous tumors and ascites, most commonly arising from mucinous tumors of the appendix, however, the ovary or the colon may be the primary site of origin. The tumor is not harmful by itself, but the mucus accumulation in abdominal cavity compresses vital organs such as spleen, kidney, colon. On 1842, Carl F. Rokitansky described the first case of<unk> .<unk>  may be divided into two pathological subtypes with different etiology and prognosis, these two subtypes are<unk> l adenomucinosis and<unk> l mucinous carcinoma. The K-Ras and p53 genes are involved in the oncogenesis.<unk>  must be differentiated from<unk> l carcinomatosis without mucinous ascites,<unk> l sarcomatosis, and tuberculosis<unk> tis. The incidence of<unk>  is approximately 0.1 person per 100,000 individuals worldwide. Females are more commonly affected with<unk>  than males. The median age at diagnosis is 50 years. There are no established risk factors for<unk> . Patients with<unk>  may develop abdominal or pelvic pain, bloating, abdominal distension, weight change, and infertility symptoms if left untreated. Common physical examination findings of<unk>  include abdominal tenderness, abdominal distention. On abdominal CT scan,<unk>  is characterized by low attenuation, loculated ascitic mucinous fluid in the<unk> m, omentum and mesentery with scalloping of visceral surfaces of the liver. On abdominal MRI,<unk>  is characterized by a mass which is hypointense on T1-weighted MRI and hyperintense on T2-weighted MRI. Finding on ultrasound scan suggestive of<unk>  are echogenic<unk> l masses or ascites which is not mobile. Cytoreductive surgery combined with hyperthermic intraperitoneal chemoperfusion is the optimal way of treatment for<unk> .
Pseudomyxoma peritonei
Primary peritoneal cancer
Peritoneal carcinomatosis
Cholangiocarcinoma
Postcholecystectomy syndrome
Splenic cyst
Sclerosing encapsulating peritonitis
Pyogenic liver abscess