Liver transplantation is the final treatment for patients with metabolic disease associated associated with GSD type 1. Indications for liver transplantation include patients with multifocal lesions, growing lesions that do not regress with improved dietary regimens, and patients who do not have evidence of distant metastatic disease. There is resolution of metabolic derangements (correction of hypoglycemia, lactic acidosis, hyperuricemia, and hyperlipidemia) after liver transplantation in patients with GSD type 1.
Glycogen storage disease type I surgery
Glycogen storage disease type III surgery
Glucose-6-phosphate dehydrogenase deficiency surgery
Hemochromatosis surgery
Zollinger-Ellison syndrome surgery
Tropical sprue surgery
Glycogen storage disease type III medical therapy
Glycogen storage disease type I medical therapy