<unk>  is a type of rare benign kidney tumor. On gross pathology, large, unilateral, multiloculated, and well-encapsulated<unk>  tumor is the characteristic finding of<unk> . On microscopic histopathological analysis, cysts lined by a simple epithelium with a hobnail morphology and ovarian-like stroma are characteristic findings of<unk> .<unk>  is caused by mutations in the DICER1 gene.<unk>  must be differentiated from Wilm's tumor, renal cell carcinoma,<unk>  mesoblastic nephroma, and autosomal recessive polycystic kidney disease.<unk>  is a rare disease that tends to affect paediatric population and individuals in the 5th - 6th decades. In paediatric population, males are more commonly affected with<unk>  than females. In later life, females are more commonly affected with<unk>  than males.<unk> s are often asymptomatic. Possible symptoms of<unk>  include hematuria, urinary frequency, and dysuria. Biopsy is helpful in the diagnosis of<unk> . Surgery is the mainstay of treatment for<unk> . Common complications of<unk>  include infection, urinary tract obstruction, hemorrhage, and rupture. Prognosis is generally excellent.
Cystic nephroma
Mesoblastic nephroma
Medullary sponge kidney
Renal cyst
Multicystic dysplastic kidney
Renal oncocytoma
Horseshoe kidney
Medullary cystic kidney disease