<unk>  is to a condition of unusual and asymmetrical gonadal development  leading to an unassigned sex differentiation. A number of differences have been reported in the karyotype, most commonly a mosaicism  45,X/ 46, XY. If  Turner syndrome is defined as a condition where one sex chromosome is absent or abnormal,<unk>  may be interpreted as a specific variation of Turner’s. The phenotypical expression  may be ambiguous, intersex, or male, or female pending the extent of the mosaicism.
It has been pointed out that the gonads may not be symmetrical, thus the development of the Mullerian duct and wolffian duct may be asymmetrical, too.  The presence of dysgenetic gonadal tissue and Y chromosome material, there is a high risk of the development of a gonadoblastoma, thus removal of the gonads is usually indicated.
Mixed gonadal dysgenesis
XX gonadal dysgenesis
Gonadal dysgenesis
Cryptorchidism
Androgen insensitivity syndrome
Mullerian dysgenesis
Supernumerary kidney
Pseudohermaphroditism