<unk>  is an inherited disorder that causes ammonia and other toxic substances to accumulate in the blood. Two forms of<unk>  have been described; they have different signs and symptoms and are caused by mutations in different genes.<unk>  belongs to a class of genetic diseases called urea cycle disorders. The urea cycle is a sequence of chemical reactions that takes place in the liver. These reactions process excess nitrogen, generated when protein is used by the body, to make a compound called urea that is excreted by the kidneys.
Both types of<unk>  are inherited in an autosomal recessive pattern.
Citrullinemia
Hyperinsulinism
D-Glyceric acidemia
Idiopathic hypoglycemia
Ketotic hypoglycemia
Hypertryptophanemia
Stress hyperglycemia
Isovaleric acidemia