<unk>  <unk> , also known as<unk>  aciduria") is an inborn error of intermediary metabolism that may present in the early neonatal period with progressive encephalopathy and death due to a secondary hyperammonemia.<unk>  does not always result in death, if it is diagnosed at an early age.
Methylmalonic acidemia
Phenylketonuria
Familial hyperchylomicronemia
Alkaptonuria
Mevalonic aciduria
3-Methylglutaconic aciduria
Homocystinuria
Galactosemia