<unk>  is a a rare, slow-growing, histologically benign intracranial tumor that is commonly located in the ventricular system of the choroid<unk> . It may obstruct the cerebrospinal fluid flow, causing elevated intracranial pressure.<unk>  is neuroectodermal in origin and similar in structure to a normal choroid<unk> . They may be created by epithelial cells of the choroid<unk> .<unk>  may be associated with Aicardi syndrome, Von Hippel-Lindau disease, and Li-Fraumeni syndrome. On gross pathology,<unk>  is characterized by a soft, solid, pink to red, capsulated, vascular, and friable cauliflower-like mass. On microscopic histopathological analysis,<unk>  is characterized by papillary structures with a delicate fibrovascular core lined by columnar or cuboidal epithelial cells with vesicular nuclei. Its appearance is very similar to normal choroid<unk> .<unk>  is demonstrated by positivity to tumor marker such as cytokeratin (CK7).<unk>  may be differentiated from choroid<unk>  carcinoma, choroid<unk>  metastasis, medulloblastoma, and intraventricular meningioma.<unk>  accounts for approximately 1% of all brain tumors, 2-6% of all pediatric brain tumors, and 0.5% of the adult brain tumors.<unk>  is a rare disease that tends to affect children and adults. Males are more commonly affected with<unk>  than females. The male to female ratio is approximately 2.8 to 1. If left untreated, patients with<unk>  may progress to develop seizures, hydrocephalus, focal neurological deficits, cranioneuropathies, psychosis, and coma. Common complications of<unk>  include CSF seeding, obstructive hydrocephalus, blindness, psychosis, and coma. The prognosis is excellent, and the 5-year survival rate after complete excision of<unk>  is approximately 100%. Symptoms of<unk>  include headache, vomiting, seizures, and vision loss. Common physical examination findings of<unk>  include bulging fontanelle, enlarged head size, papilledema, altered mental status, and cranioneuropathies (6th and 7th nerve palsy). Head CT scan and brain MRI are helpful in the diagnosis of<unk> . On CT scan,<unk>  is characterized by iso- to hyperdense well-defined lobulated masses with intense homogenous enhancement and associated hydrocephalus. If there is markedly heterogeneous contrast enhancement, a choroid<unk>  carcinoma should be suspected. On MRI,<unk>  is characterized by a well demarcated, extra-axial mass that is iso- to hypointense on T1-weighted imaging and iso- to hyperintense on T2-weighted imaging. On contrast administration, there is generally marked homogenous enhancement. The predominant therapy for<unk>  is surgical resection. Radiotherapy is indicated for the inoperable residual tumor or resistant/aggressive subtype, whereas chemotherapy is reserved for the recurrent tumors.
Choroid plexus papilloma
Choroid plexus tumor
Craniopharyngioma
Acoustic neuroma
Ganglioneuroma
Choroidal fissure cyst
Arachnoid cyst
Spiradenoma