<unk>  is a benign tumor arising within the ventricles of the brain. It is almost exclusively associated with tuberous sclerosis, an autosomal dominant disorder associated with the inactivation of the tumor suppressor genes, TSC1 and/or TSC2.<unk>  is believed to arise from a<unk>  nodule present in the ventricular wall of a patient with tuberous sclerosis. On microscopic histopathological analysis, it is characterized by pleomorphic multinuleated eosinophilic<unk> s with abundant cytoplasm, arranged in a perivascular pseudopallisading pattern.<unk>  is a disease that tends to affect the pediatric, adolescent, and young adult population. Males are more commonly affected than females. According to the International Tuberous Sclerosis Complex Consensus, screening for<unk>  by MRI is recommended every 1-3 years among patients with tuberous sclerosis, even in the absence of symptoms. If left untreated, patients with<unk>  may progress to develop seizures, occlusion of the foramen of Monro with subsequent elevated intracranial pressure and obstructive hydrocephalus, infection, stroke, and death. Common complications of<unk>  include obstructive hydrocephalus, intratumoral hemorrhage, and infection. Symptoms of<unk>  include headache, seizures, vision loss, changes in speech, weakness in limbs, and sensory loss. Common physical examination findings of<unk>  include papilledema, vision field defects, developmental delay, aphasia, sensory loss, and hemiparesis. Head CT scan and brain MRI may be helpful in the diagnosis of<unk> . On head CT scan,<unk>  is characterized by an intraventricular mass near the foramen of Monro, which is iso- or slightly hypoattenuating to the grey matter. Accompanying hydrocephalus may be present. There is marked enhancement on contrast administration. On MRI,<unk>  is characterized by hypo- to isointensity on T1-weighted imaging and hyperintensity on T2-weighted imaging. There may be marked enhancement on contrast administration. Surgical resection is the mainstay treatment of<unk>  but in certain cases, medical therapy such as everolimus is used.
Subependymal giant cell astrocytoma
Protoplasmic astrocytoma
Gemistocytic astrocytoma
Oligoastrocytoma
High grade astrocytoma
Hemangiopericytoma
Ganglioglioma
Hemangioblastoma