<unk>  was first discovered by Fischer in 1913.<unk>  is classified into 2 distinct types: classic and differentiated (Osteofibrous dysplasia (OFD) - like).<unk>  is a low grade, malignant bone tumor. This tumor is predominantly located in tibia ( most in mid-portion of tibia). Most locations of the tumor include tibia, ipsilateral fibula, humerus, ulna, femur, fibula. It is a Yellow gray or grayish white tumor. In microscopic examination admixture of both epithelial and osteofibrous component can be seen.<unk>  may be caused by displacement of basal epithelium of skin during embryogenesis, traumatic implantation.<unk>  is a rare bone cancer ( 0.1–0.5% of all primary bone tumors ). Risk factors in the development of<unk>  may include benign osteofibrous dysplasia. If left untreated, 15-30% of patients with<unk>  may metastasize to other parts of the body such as lungs or nearby lymph nodes. The diagnosis of<unk>  is based on the findings of radiologic studies such as x-ray, CT, and MRI. The most common symptoms of<unk>  include swelling with or without pain. Less common symptoms of<unk>  include pathological fracture.<unk>  may present with bowing deformity of the tibia. There is no medical therapy for<unk> . Radiation therapy and chemotherapy are not effective. Surgery is the mainstay of treatment for<unk> .
Adamantinoma
Hamartoma
Cylindroma
Esthesioneuroblastoma
PEComa
Syringoma
Neuroma
Neurofibroma