<unk>  is an autosomal recessive variant of ARVD, described initially on the Greek island of<unk> .  There, the penetrance is >90%.
It involves the gene that codes for plakoglobin (a protein that is involved in cellular adhesion), on chromosome 17p.<unk>  is described as a triad of ARVD, palmoplantar keratosis, and wooly hair.
The signs of<unk>  are more severe than with autosomal dominant ARVD.
Naxos disease
Kennedy disease
Pickardt syndrome
Shy-Drager syndrome
Spinal muscular atrophy other forms
Tay-Sachs disease
Huntington's disease
Lesch-Nyhan syndrome