<unk>  is a congenital error of an enzyme in the citric acid cycle.  It is thought to be caused by low molar ratios of ketone bodies in the plasma of neonates with congenital lactic acidosis.  The lactic acidosis and low ketone body concentration indicate a dysfunction in the citric acid cycle.
Alpha-ketoglutarate dehydrogenase deficiency
Pyruvate kinase deficiency
Pyruvate dehydrogenase deficiency
Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
Carbamoyl phosphate synthetase I deficiency
Very long-chain acyl-coenzyme A dehydrogenase deficiency
Aldolase A deficiency
ALA dehydratase deficiency