<unk>  is a very rare subtype of diffuse<unk>  B-cell lymphoma (DLBCL). It is also considered a distinct type of non-Hodgkin lymphoma (NHL) in the World Health Organization (WHO) classification system.<unk>  affects small blood vessels.  It is a rare and aggressive variant of<unk>  proliferation of clonal lymphocytes with little to no parenchymal involvement. Based on the clinical presentation,<unk>  may be classified into either Western variant or Asian variant. On microscopic histopathological analysis, diffuse infiltrate of<unk>  atypical<unk> s with irregular nuclear contours, vesicular chromatin, and occasional prominent nucleoli  are characteristic findings of<unk> . The incidence of<unk>  increases with age; the median age at diagnosis is 67 years.<unk>  affects men and women equally. People with this type of lymphoma often have a poor prognosis. Symptoms of the<unk>  include fever, weight loss, night sweats, chest pain, abdominal pain, bone pain, and painless swellings in the neck, axilla, groin, thorax, and abdomen. Lymph node biopsy is diagnostic of<unk> . CT, MRI, and PET scan may be helpful in the diagnosis of<unk> . The predominant therapy for<unk>   is chemotherapy. Adjunctive radiotherapy may be required.
Intravascular large B-cell lymphoma
Clear cell sarcoma of the kidney
Diffuse large B cell lymphoma
Kaposiform hemangioendothelioma
Lymphoplasmacytic lymphoma
Waldenström's macroglobulinemia
Follicular lymphoma
Desmoplastic small round cell tumor