A 10–year old male child was presented to the pediatrician for evaluation of a seizure disorder. On examination a vascular plaque was found along the ophthalmic and maxillary divisions of the trigeminal nerve. The mother informed the pediatrician that the lesion was present since birth and there was no change in morphology. The most likely possibility is –
(A) Sturge Weber syndrome (B) Infantile hemangioma (C) Congenital hemangioma (D) Proteus syndrome
(A) This child has :


Seizure disorder
Vascular plaque along the ophthalmic and maxillary divisions of trigeminal nerve
Lesion presenting since birth and not chonging in morphology


The diagnosis is sturge weber syndrome.
Sturge weber syndrome is a rare congenital vascular disorder characterized by facial capillary malformation (port wine stain) and associated capillary venous malformation affecting the brain and eye.
It consists of angiomas involving the leptomeninges and skin of face typically in the ophthalmic and maxillary distributions of trigeminal nerve.