PAINLESS UNILATERAL PROPTOSIS PRESENTING AS EWING'S SARCOMA- A RARE CASE REPORT

Ewing's sarcoma is a part of a spectrum of the Ewing family of soft tissue tumors that have a primitive neuro-ectodermal
origin most commonly originating from the appendicular and axial skeleton. Occurrence in the orbit is a rare presentation.
case report a 15-year-old girl presented with painless unilateral swelling of the right eye since 4 months on histopathological examination came
out to be a small round cell tumor with primitive neuroendocrine origin. she was started on chemotherapy with VAC+IE regimen as induction
chemotherapy but as the disease was progressive and not responding after 17 cycles of alternating VAC+IE second-line chemotherapy with
irinotecan and temozolomide was started and after three cycles surgery was deferred i/v/o intracranial extension so she was treated with external
beam radiotherapy 59.4gy in 33#'s at 1.8gy/# with concurrent irinotecan and temozolomide with complete response after radiotherapy. she was on
follow-up for 4 months and was later diagnosed with secondary deposits in the lung which she could not cave in and expired.