Glycoproteinosis
# Glycoproteinosis

Glycoproteinosis are lysosomal storage diseases affecting glycoproteins, resulting from defects in lysosomal function. The term is sometimes reserved for conditions involving degradation of glycoproteins.

## Types

* (E77.0) Defects in post-translational modification of lysosomal enzymes
   * Mucolipidosis II (I-cell disease)
   * Mucolipidosis III (pseudo-Hurler polydystrophy)
* (E77.1) Defects in glycoprotein degradation
   * Aspartylglucosaminuria
   * Fucosidosis
   * Mannosidosis
   * Sialidosis (mucolipidosis I)

Another type, recently characterized, is galactosialidosis.

